Idiopathic catastrophic epileptic encephalopathy: an untreatable convulsive malady in infancy

To present a case of catastrophic childhood epileptic syndrome with multifocal status epilepticus. A 4 years old boy with a multifocal status epilepticus of unknown origin which could only be controlled along some days with thiopentone enough to cause electrical suppression, and relapsed again after...

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Bibliographic Details
Published in:	Revista de neurologiá Vol. 38; no. 10; pp. 931 - 934
Main Authors:	Prats-Viñas, J M, Pilar-Orive, J, García-Pérez, R, Martínez-González, M J, García-Ribes, A
Format:	Journal Article
Language:	Spanish
Published:	Spain 16-05-2004
Subjects:	Anticonvulsants - therapeutic use Atrophy - pathology Barbiturates - therapeutic use Brain - pathology Brain - physiopathology Child, Preschool Disease Progression Electroencephalography Humans Infant Magnetic Resonance Imaging Male Status Epilepticus - drug therapy Status Epilepticus - pathology Status Epilepticus - physiopathology
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Summary:	To present a case of catastrophic childhood epileptic syndrome with multifocal status epilepticus. A 4 years old boy with a multifocal status epilepticus of unknown origin which could only be controlled along some days with thiopentone enough to cause electrical suppression, and relapsed again after having stopped it. But for very high doses of barbiturates, any antiepileptic drug could control or improve the convulsions. MRI, initially normal, was followed by a progressive cerebral and cerebellar atrophy and the boy survived with heavy neurological secuelae.
Bibliography:	ObjectType-Article-2 SourceType-Scholarly Journals-1 ObjectType-Feature-1 content type line 23 ObjectType-Report-3 ObjectType-Case Study-4
ISSN:	0210-0010