Kartagener syndrome with abnormalities of cilia

Kartagener syndrome of sinusitis, bronchiectasis and situs inversus has been so called since his classical description in 1933. This report presents two further cases, a brother and sister. They were extensively studied and the findings are reported. A unique finding was that in both patients, both...

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Bibliographic Details
Published in:	Journal of otolaryngology Vol. 7; no. 2; p. 95
Main Authors:	Lupin, A J, Misko, G J
Format:	Journal Article
Language:	English
Published:	Canada 01-04-1978
Subjects:	Adolescent Aged Bronchi - pathology Bronchi - ultrastructure Bronchiectasis - pathology Child Child, Preschool Cilia - pathology Cilia - ultrastructure Female Humans Infant Kartagener Syndrome - genetics Kartagener Syndrome - pathology Male Maxillary Sinus - pathology Maxillary Sinus - ultrastructure Mucous Membrane - pathology Mucous Membrane - ultrastructure Sinusitis - pathology
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Summary:	Kartagener syndrome of sinusitis, bronchiectasis and situs inversus has been so called since his classical description in 1933. This report presents two further cases, a brother and sister. They were extensively studied and the findings are reported. A unique finding was that in both patients, both in the maxillary sinuses and in the bronchi, abnormal cilia were discovered on electron microscopy. After a search of the literature the authors conclude that this finding is probably congenital rather than acquired and may explain the development of the sinusitis and bronchiectasis.
ISSN:	0381-6605