What surgery for recurrent Darier-Ferrand sarcoma of the chest wall?

• Published in: Revue de pneumologie clinique Vol. 73; no. 2; pp. 100 - 105
• Main Authors: Rabiou, S, Ouadnouni, Y, Efared, B, Belliraj, L, Issoufou, I, Ammor, F Z, Ghalimi, J, Lakranbi, M, Sani, R, Oufkir, A, Smahi, M
• Format: Journal Article
• Language: French
• Published: France 01-04-2017
• Subjects: Adult; Dermatofibrosarcoma - pathology; Dermatofibrosarcoma - surgery; Humans; Male; Middle Aged; Neoplasm Recurrence, Local - surgery; Sarcoma - pathology; Sarcoma - surgery; Skin Neoplasms - pathology; Skin Neoplasms - surgery; Skin Transplantation; Thoracic Surgical Procedures - methods; Thoracic Wall - pathology; Thoracic Wall - surgery; Chest wall tumor; Recurrence; Récidive; Dermatofibrosarcoma protuberans of the chest wall; Surgery; Chirurgie; Soft tissue sarcoma; Sarcome de Darrier-Ferrand; Tumeur de la paroi thoracique; Sarcome de tissu mou
• ISSN: 0761-8417
• DOI: 10.1016/j.pneumo.2016.09.005

Dermatofibrosarcoma protuberans (Darrier-Ferrand sarcoma, DFSP) is an uncommon tumor. This sarcoma has a tendency to local recurrence, requiring a wide surgical resection.
We report herein two cases of patients presenting with recurrent dermatofibrosarcoma protuberans after several surgical resections. A wide surgical resection with guided tissue regenaration has been performed in one case, whereas the second case required a skin graft.
Despite a short follow-up, our aim was to highlight the local aggressiveness of the DFSP and point out its therapeutic challenge, usually requiring a wide and aggressive surgery.