Melanotic neuroectodermal tumor of infancy: case report and review of the literature

Melanotic Neuroectodermal Tumor of Infancy (MNTI) is a rare but distinct neoplastic entity in infancy. Diagnosis is usually made before the age of 12 months. The common clinical presentation is a rapidly growing mass of the pre-maxillary area. Its surface is unevenly pigmented. To affirm the diagnos...

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Bibliographic Details
Published in:	Revue de laryngologie - otologie - rhinologie Vol. 132; no. 3; p. 173
Main Authors:	Camuzard, O, Rosello, O, Maschi, C, Castillo, L, Deville, A, Boyer, C, Chevallier, A, Bailleux, S
Format:	Journal Article
Language:	English
Published:	France 2011
Subjects:	Female Follow-Up Studies Humans Infant Maxillary Neoplasms - pathology Maxillary Neoplasms - surgery Neuroectodermal Tumor, Melanotic - pathology Neuroectodermal Tumor, Melanotic - surgery Treatment Outcome
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Summary:	Melanotic Neuroectodermal Tumor of Infancy (MNTI) is a rare but distinct neoplastic entity in infancy. Diagnosis is usually made before the age of 12 months. The common clinical presentation is a rapidly growing mass of the pre-maxillary area. Its surface is unevenly pigmented. To affirm the diagnosis a biopsy is necessary. Few cases of malignancy have been described (5% of cases). Adequate surgical excision is the treatment of choice. Recurrence rate is about 10 to 15% within 5 years. We report in this article the case of a newborn with MNTI illustrating that an R0 surgical excision can be correlated to a favourable prognosis. In this case the 5 years follow up didn't show any local or distant recurrence.
ISSN:	0035-1334