Poland Syndrome- A Rare Congenital Condition

Poland Syndrome- A Rare Congenital Condition

Named after Sir Alfred Poland, Poland syndrome is a rare congenital anomaly classically characterized by the absence of unilateral chest wall muscles and sometimes ipsilateral symbrachydactyly (abnormally short and webbed fingers). The aetiology is probably a vascular disruption sequence of the subc...

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Bibliographic Details
Published in:Journal of Bangladesh College of Physicians & Surgeons Vol. 36; no. 4; pp. 166 - 169
Main Authors: Hossain, Homayra Tahseen, Khandaker, Md Abul Kashem, Islam, Quazi Tarikul, Ahasan, HAM Nazmul, Adnan, Munshi MB Md Shoaib, Islam, Nazmul
Format: Journal Article
Language:English
Published: Dhaka Bangladesh College of Physicians & Surgeons 01-10-2018
Subjects:
Congenital diseases
Musculoskeletal diseases
Bangladesh
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Summary:Named after Sir Alfred Poland, Poland syndrome is a rare congenital anomaly classically characterized by the absence of unilateral chest wall muscles and sometimes ipsilateral symbrachydactyly (abnormally short and webbed fingers). The aetiology is probably a vascular disruption sequence of the subclavian arteries. In most cases, Poland Syndrome is sporadic. We report a 26 year old male patient with typical features of Poland Syndrome associated with bronchiectasis and mitral valve prolapse- a very rare association. To the best of our knowledge, this is the first documented case of a Poland Syndrome with rare association reported from Bangladesh.J Bangladesh Coll Phys Surg 2018; 36(4): 166-169
ISSN:1015-0870
2309-6365
DOI:10.3329/jbcps.v36i4.38186