A case of dorsal agenesis of pancreas associated with unilateral renal agenesis, unicornuate uterus, and ovarian ectopia: A brief review and learning points

• Published in: The Indian journal of radiology & imaging Vol. 30; no. 3; pp. 395 - 399
• Main Authors: Bhandari, Arindam, Mandal, Samrat
• Format: Journal Article
• Language: English
• Published: A-12, Second Floor, Sector -2, NOIDA -201301, India Thieme Medical and Scientific Publishers Private Ltd 01-07-2020; Wolters Kluwer India Pvt. Ltd; Medknow Publications and Media Pvt. Ltd; Georg Thieme Verlag Stuttgart; Wolters Kluwer - Medknow; Thieme Medical and Scientific Publishers Pvt. Ltd
• Subjects: Anomalies; Care and treatment; Case Report; Case studies; Complications and side effects; Development and progression; dorsal agenesis of pancreas; ectopic ovary; Female genital diseases; Kidney diseases; Literature reviews; Organs; Pancreas; Pancreatic diseases; unicornuate uterus; unilateral renal agenesis; Uterus; Visualization; India; Dorsal agenesis of pancreas; ectopic ovary; unicornuate uterus; unilateral renal agenesis
• ISSN: 0971-3026; 0970-2016; 1998-3808; 0971-3026
• DOI: 10.4103/ijri.IJRI_165_19

Abstract
Dorsal agenesis of the pancreas is a rare entity, with about 100 cases reported. It can be overlooked on ultrasound due to the non visualization of the body and tail of the pancreas.This is due to overlying gas in the stomach, which offers a poor acoustic window and obscures visualization. Renal agenesis and Mullerian duct anomalies are uncommon associations of dorsal agenesis of the pancreas because of the separate embryological origin of the pancreas and genitourinary organs. Here, we present a case of a 17-year-old patient who had dorsal agenesis of the pancreas, associated with unilateral renal agenesis, unicornuate uterus, and ectopic ovary. We describe the anomalies and discuss the radiological differential diagnosis and potential pitfalls. We provide a brief review of the literature with few radiological teaching points and possible genetic implications of the case.