Danon Disease with Internal Carotid Artery Occlusion Showing Good Clinical Outcome Due to Robust Collaterals

• Published in: Annals of the Indian Academy of Neurology Vol. 23; no. 1; pp. 139 - 140
• Main Authors: Lee, Mi, Ku, Bon, An, Sang, Kim, Hyeyun, Lee, Su-Jin, Kim, YeongIn
• Format: Journal Article
• Language: English
• Published: India Wolters Kluwer India Pvt. Ltd 01-01-2020; Medknow Publications and Media Pvt. Ltd; Medknow Publications & Media Pvt. Ltd; Medknow Publications & Media Pvt Ltd; Wolters Kluwer Medknow Publications
• Subjects: Aphasia; Arrhythmia; Atrial fibrillation; Blood flow; Cardiomyopathy; Carotid arteries; Carotid artery; Cerebral blood flow; Clinical outcomes; Computed tomography; Death; Dilated cardiomyopathy; Disabilities; Echocardiography; Electrocardiography; Fibrillation; Heart; Hypertrophy; Ischemia; Letters to the Editor; Meninges; Myocardial diseases; Patient outcomes; Patients; Splenomegaly; Stroke; Sudden cardiac death; Thromboembolism; Veins & arteries; Ventricle; Wolff-Parkinson-White syndrome
• ISSN: 0972-2327; 1998-3549
• DOI: 10.4103/aian.AIAN_244_19

Transthoracic echocardiography demonstrated a severe left ventricular hypertrophy and depressed left ventricular ejection fraction of 23% [Figure 1] and Video]. The brain computed tomographic angiogram revealed occlusion of the left proximal ICA with faint blood flow from the M2 portion of the left middle cerebral artery, mainly supplied by the posterior cerebral artery (PCA) and leptomeningeal collaterals [Figure 2]. The risk stratification of patients with dilated cardiomyopathy may help determine which patients will have the largest net clinical benefit from long-term anticoagulation.