Echocardiographic features of cardiac amyloidosis presenting as endomyocardial disease in a 54-year-old male

• Published in: Journal of cardiology Vol. 54; no. 1; pp. 162 - 166
• Main Authors: Fealey, Michael E, Edwards, William D., MD, Buadi, Francis K., MD, Syed, Imran S., MD, Grogan, Martha, MD
• Format: Journal Article
• Language: English
• Published: Netherlands Elsevier Ltd 01-08-2009
• Subjects: Amyloidosis - diagnostic imaging; Cardiac amyloidosis; Cardiomyopathies - diagnostic imaging; Cardiovascular; Diagnosis, Differential; Echocardiography; Endomyocardial disease; Endomyocardial Fibrosis - diagnosis; Humans; Male; Middle Aged; Cardiac amyloidosis; Endomyocardial disease; Echocardiography
• ISSN: 0914-5087; 1876-4738
• DOI: 10.1016/j.jjcc.2008.11.002

Summary Although primary cardiac amyloidosis is a rare affliction of the heart, its clinical and pathology features have been well described. Patients generally present with exertional dyspnea, chest discomfort, or congestive heart failure. Cardiac imaging typically reveals ventricular wall thickening, systolic and diastolic dysfunction, valvular thickening, and pericardial effusion. In the case reported herein, a patient with suspected cardiac amyloid demonstrated electrocardiographic and echocardiographic findings that were not only inconsistent with typical depositional patterns, but also potentially suggestive of endomyocardial disease.