The ultrasound findings in a rare case of Nutcracker syndrome, Wilkie's syndrome, and Dunbar syndrome combination

• Published in: Journal of medical ultrasound Vol. 31; no. 1; pp. 55 - 59
• Main Authors: Pennisi, Isabella, Farina, Renato, Foti, Pietro, Basile, Antonio
• Format: Journal Article
• Language: English
• Published: India Wolters Kluwer India Pvt. Ltd 01-01-2023; Wolters Kluwer - Medknow; Wolters Kluwer Medknow Publications
• Subjects: cardiovascular abnormalities; Case Report; color-doppler ultrasound; dunbar syndrome; nutcracker syndrome; color-Doppler ultrasound; Dunbar syndrome; Nutcracker syndrome; Cardiovascular abnormalities
• ISSN: 0929-6441; 2212-1552
• DOI: 10.4103/jmu.jmu_211_21

Vascular compression syndromes represent a group of rare and poorly understood diseases. Dunbar syndrome (DS) is caused by the median arcuate ligament of diaphragm originating lower than normal and causing compression of celiac artery. The Nutcracker is caused by the superior mesenteric artery (SMA) originating from aorta at an acute angle causing a restriction of aortomesenteric space that is traversed by the left renal vein and duodenum; if the compression involves only the left renal vein and becomes symptomatic it is called Nutcracker syndrome; if the symptomatic compression involves only the duodenum it is called Wilkie's syndrome or SMA syndrome. The knowledge of these rare pathologies is essential to reduce the false negatives which still remain very high; it is, therefore, necessary to promote greater knowledge as the lack of diagnosis can be very dangerous for the patient's health. We describe a rare case of a combination of DS, Nutcracker, and SMA or Wilkie's syndrome in a young patient.