CONGENITAL ABSENCE OF UTERUS
These are two case reports of females with primary amenorrhea, well developed secondary sexual characteristics and congenital absence of uterus. The incidence of Mayer-Rokitansky-Kuester-Hauser syndrome was not clearly established, but studies indicate a variation of 1/4,000 and 1/5,000 live births...
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Published in: | Gomal journal of medical sciences Vol. 17; no. 1; pp. 24 - 26 |
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Main Author: | |
Format: | Journal Article |
Language: | English |
Published: |
Knowledge Bylanes
31-03-2019
Gomal Medical College, D.I.Khan, Pakistan |
Subjects: | |
Online Access: | Get full text |
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Summary: | These are two case reports of females with primary amenorrhea, well developed secondary sexual characteristics and congenital absence of uterus. The incidence of Mayer-Rokitansky-Kuester-Hauser syndrome was not clearly established, but studies indicate a variation of 1/4,000 and 1/5,000 live births of the female sex. The syndrome is characterized by aplasia of the Müllerian duct (uterus and upper two-thirds of the vagina) on a person who has karyotype 46, XX with female phenotype characteristic of primary amenorrhea in adolescence. Treatment is usually delayed until the patient is ready to begin sexual activity. |
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ISSN: | 1819-7973 1997-2067 |
DOI: | 10.46903/gjms/17.01.2015 |