Uterine didelphys with duplicated upper vagina and bilateral lower vaginal agenesis: a novel Müllerian anomaly with options for surgical management

• Published in: Fertility and sterility Vol. 89; no. 3; pp. 693 - 698
• Main Authors: Growdon, Whitfield B., M.D, Laufer, Marc R., M.D
• Format: Journal Article
• Language: English
• Published: New York, NY Elsevier Inc 01-03-2008; Elsevier Science
• Subjects: Adolescent; bicollis; Biological and medical sciences; Child; Contraceptives, Oral - therapeutic use; Female; Female genital diseases; Gynecologic Surgical Procedures; Gynecology. Andrology. Obstetrics; Humans; Internal Medicine; Magnetic Resonance Imaging; Medical sciences; Mullerian Ducts - abnormalities; Mullerian Ducts - pathology; Mullerian Ducts - surgery; Non tumoral diseases; novel congenital anomaly; Obstetrics and Gynecology; Surgically-Created Structures; Treatment Outcome; Uterus - abnormalities; Uterus - pathology; Uterus - surgery; Uterus didelphys; Vagina - abnormalities; Vagina - pathology; Vagina - surgery; vaginal agenesis of the lower vagina; vaginal atresia; vaginal atresia; novel congenital anomaly; bicollis; Uterus didelphys; vaginal agenesis of the lower vagina; Agenesis; Congenital; Gynecology; Uterus didelphis; Vagina; Bilateral; Congenital disease; Obstetrics; Female genital diseases; Treatment; Malformation; Surgery; Mullerian duct; Uterine diseases; Atresia; Anomaly
• ISSN: 0015-0282; 1556-5653
• DOI: 10.1016/j.fertnstert.2007.03.062

Objective To describe a novel Müllerian anomaly and management options. Design Case series report. Setting Metropolitan tertiary care children's hospital. Patient(s) Three caucasian girls, aged 12, 13, and 15 years, with a novel congenital anomaly. Intervention(s) Interval staged vaginoplasties. Main Outcome Measure(s) Functional vagina. Result(s) Didelphys Müllerian development with vaginal duplication and agenesis of both lower vaginas with staged vaginoplasties resulting in normal functional vaginas. Conclusion(s) Staged pull-through vaginoplasties led to functional outcome in this unusual anomaly.