Pleuropulmonary blastoma in congenital cystic adenomatoid malformation: report of a case

• Published in: European journal of pediatric surgery Vol. 11; no. 3; p. 196
• Main Authors: Federici, S, Domenichelli, V, Tani, G, Sciutti, R, Burnelli, R, Zanetti, G, Dòmini, R
• Format: Journal Article
• Language: English
• Published: United States 01-06-2001
• Subjects: Antineoplastic Combined Chemotherapy Protocols - therapeutic use; Biopsy, Needle; Cell Transformation, Neoplastic - pathology; Child, Preschool; Cystic Adenomatoid Malformation of Lung, Congenital - diagnosis; Cystic Adenomatoid Malformation of Lung, Congenital - pathology; Follow-Up Studies; Humans; Lung Neoplasms - diagnosis; Lung Neoplasms - drug therapy; Lung Neoplasms - pathology; Magnetic Resonance Imaging; Male; Pulmonary Blastoma - diagnosis; Pulmonary Blastoma - drug therapy; Pulmonary Blastoma - pathology; Tomography, X-Ray Computed
• ISSN: 0939-7248
• DOI: 10.1055/s-2001-15490

Pulmonary blastoma is a rare malignant tumor seen in both adults and children. Approximately only 25% of cases occur in pediatric patients, many of whom affected by a congenital pulmonary cystic lesion. The clinical features, radiological findings and management of a 3-year-old boy affected by a pulmonary blastoma which arose in a congenital cystic adenomatoid malformation are reported, and an extensive review of the literature is also made. Because of the well-known tendency of cystic pulmonary diseases to develop malignancies, authors recommend the surgical excision of these kind of lesion or at least their close radiological follow-up.