Lung Transplantation in a Patient with COPA Syndrome

Lung Transplantation in a Patient with COPA Syndrome

COPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral...

Full description

Saved in:
Bibliographic Details
Published in:Case reports in transplantation Vol. 2020; no. 2020; pp. 1 - 2
Main Authors: Erasmus, David, Khoor, Andras, Kornafeld, Anna, Mallea, Jorge M.
Format: Journal Article
Language:English
Published: Cairo, Egypt Hindawi Publishing Corporation 2020
Hindawi
John Wiley & Sons, Inc
Hindawi Limited
Subjects:
Arthritis
Autoimmunity
Case Report
Case reports
Diseases
Gastroesophageal reflux
Gene mutations
Genetic aspects
Health risk assessment
Hemorrhage
Lung diseases
Lungs
Mutation
Patients
Pneumonia
Proteins
Relapse
Transplantation of organs, tissues, etc
Transplants & implants
Online Access:Get full text
Tags: Add Tag
No Tags, Be the first to tag this record!
Description
Summary:COPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral lung transplant for COPA syndrome. At 15 months posttransplant, her pulmonary function is stable with no episodes of acute cellular- or antibody-mediated rejection and no evidence of disease recurrence.
Bibliography:Academic Editor: Federica Meloni
ISSN:2090-6943
2090-6951
DOI:10.1155/2020/3624795