Nevoid basal cell carcinoma syndrome

Binkley and Johnson first reported this syndrome in 1951. But it was in 1960, Gorlin-Goltz established the association of basal cell epithelioma, jaw cyst and bifid ribs, a combination which is now frequently known as Gorlin-Goltz syndrome as well as Nevoid Basal Cell Carcinoma Syndrome (NBCCS). NBC...

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Bibliographic Details
Published in:	Indian journal of dental research Vol. 17; no. 1; pp. 50 - 53
Main Authors:	Karthiga, Kannan S, Sivapatha Sundharam, B, Manikandan, R
Format:	Journal Article
Language:	English
Published:	India Medknow Publications and Media Pvt. Ltd 01-01-2006 Wolters Kluwer Medknow Publications
Subjects:	Adolescent Basal cell Carcinoma Basal Cell Nevus Syndrome - diagnosis Bifid ribs Care and treatment Case studies Dentistry Diagnosis Diagnosis, Differential Female Genetic disorders Humans Kyphoscoliosis Mandibular Diseases - diagnosis Maxillary Diseases - diagnosis Maxillary Neoplasms - diagnosis Odontogenic Cysts - diagnosis Odontogenic Keratocyst Ribs - abnormalities Spina bifida Tooth, Impacted - diagnosis Tooth, Unerupted - diagnosis India
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Summary:	Binkley and Johnson first reported this syndrome in 1951. But it was in 1960, Gorlin-Goltz established the association of basal cell epithelioma, jaw cyst and bifid ribs, a combination which is now frequently known as Gorlin-Goltz syndrome as well as Nevoid Basal Cell Carcinoma Syndrome (NBCCS). NBCCS is inherited as an autosomal dominant trait with high penetrance and variable expressivity. NBCCS is characterized by variety of cutaneous, dental, osseous, opthalmic, neurologic and sexual abnormalities. One such case of Gorlin-Goltz syndrome is reported here with good illustrations.
Bibliography:	ObjectType-Case Study-2 SourceType-Scholarly Journals-1 ObjectType-Feature-4 content type line 23 ObjectType-Report-1 ObjectType-Article-3
ISSN:	0970-9290
DOI:	10.4103/0970-9290.29891