Light chain deposition disease complicating familial Mediterranean fever

Familial Mediterranean fever (fMf) is an inherited condition characterized by polyserositis and is sometimes complicated by AA renal amyloidosis leading to nephrotic syndrome and renal failure. We present a case of a man with fMf who presented with rapidly progressive renal failure caused by light c...

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Published in:	American journal of kidney diseases Vol. 29; no. 6; p. 942
Main Authors:	Vella, J P, Doyle, G D, Campbell, E, Walshe, J J
Format:	Journal Article
Language:	English
Published:	United States 01-06-1997
Subjects:	Adult Disease Progression Familial Mediterranean Fever - complications Familial Mediterranean Fever - immunology Familial Mediterranean Fever - pathology Humans Immunoglobulin kappa-Chains - metabolism Kidney Diseases - complications Kidney Diseases - immunology Kidney Diseases - pathology Kidney Diseases - physiopathology Kidney Diseases - surgery Male
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Abstract	Familial Mediterranean fever (fMf) is an inherited condition characterized by polyserositis and is sometimes complicated by AA renal amyloidosis leading to nephrotic syndrome and renal failure. We present a case of a man with fMf who presented with rapidly progressive renal failure caused by light chain deposition disease. This disease association has not previously been described in the medical literature.
AbstractList	Familial Mediterranean fever (fMf) is an inherited condition characterized by polyserositis and is sometimes complicated by AA renal amyloidosis leading to nephrotic syndrome and renal failure. We present a case of a man with fMf who presented with rapidly progressive renal failure caused by light chain deposition disease. This disease association has not previously been described in the medical literature.
Author	Campbell, E Vella, J P Doyle, G D Walshe, J J
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SubjectTerms	Adult Disease Progression Familial Mediterranean Fever - complications Familial Mediterranean Fever - immunology Familial Mediterranean Fever - pathology Humans Immunoglobulin kappa-Chains - metabolism Kidney Diseases - complications Kidney Diseases - immunology Kidney Diseases - pathology Kidney Diseases - physiopathology Kidney Diseases - surgery Male
Title	Light chain deposition disease complicating familial Mediterranean fever
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