Airway Obstruction Management With Mandibular Distraction and Matthews Device in Pruzansky III Craniofacial Microsomia

• Published in: The Journal of craniofacial surgery Vol. 31; no. 3; pp. e277 - e280
• Main Authors: Shih, Linden, Davis, Matthew J., Sequitin, Jeromie, Abu-Ghname, Amjed, Dempsey, Robert F., Truong, Tuan A., Buchanan, Edward P.
• Format: Journal Article
• Language: English
• Published: United States by Mutaz B. Habal, MD 01-05-2020
• Subjects: Airway Obstruction - etiology; Airway Obstruction - surgery; Bone Transplantation - methods; Child, Preschool; Dentistry; Female; Goldenhar Syndrome - complications; Goldenhar Syndrome - surgery; Humans; Mandibular Diseases - etiology; Mandibular Diseases - surgery; Tracheostomy; Treatment Outcome
• ISSN: 1049-2275; 1536-3732
• DOI: 10.1097/SCS.0000000000006270

Patients with craniofacial microsomia (CFM) may present with severely malformed mandibles resulting in secondary tongue-based airway obstruction. While surgical management of clinically significant airway obstruction in these patients often involves mandibular distraction osteogenesis (MDO), patients with Pruzansky III CFM typically require additional costochondral bone grafting. In this report, the authors present the successful surgical management of airway obstruction and severe obstructive sleep apnea using a cranio-mandibular fixator (Matthews device) combined with MDO in a 4-year-old female patient with Goldenhar syndrome and associated Pruzansky III CFM. The patient tolerated the procedure without complications and experienced a significant improvement in airway obstruction. With this approach, a severely deformed mandible can be successfully distracted while avoiding tracheostomy and disruption of native TMJ anatomy.