Shone's complex with dextrocardia and situs inversus totalis: a case report

• Published in: Türk Kardiyoloji Derneği arşivi Vol. 40; no. 7; pp. 612 - 614
• Main Authors: Ekici, Berkay, Erkan, Aycan Fahri, Sökmen, Yeliz, Tüfekçioğlu, Omaç
• Format: Journal Article
• Language: English
• Published: Turkey 01-10-2012
• Subjects: Cyanosis; Dextrocardia - complications; Dextrocardia - diagnostic imaging; Dyspnea; Echocardiography; Electrocardiography; Female; Heart Murmurs; Humans; Mitral Valve - abnormalities; Mitral Valve - diagnostic imaging; Radiography, Thoracic; Situs Inversus - complications; Situs Inversus - diagnostic imaging; Young Adult
• ISSN: 1016-5169
• DOI: 10.5543/tkda.2012.70750

Parachute mitral valve complex is an unusual congenital anomaly that has been described by Shone et al. It is characterized by a parachute deformity of the mitral valve associated with additional forms of left heart anomalies, such as aortic valvular stenosis and coarctation of the aorta. A 21-year-old female who was referred to our department because of progressive dyspnea on effort and at rest and minimal cyanosis is presented in this case report. On cardiac auscultation, the patient had a grade III/VI pansystolic murmur best heard at the lower left sternal border. The chest X-ray demonstrated dextrocardia and mild cardiomegaly. Echocardiographic evaluation revealed Shone's complex, including parachute mitral valve anomaly.