Congenital cystic adenomatoid malformation with extramedullary hematopoiesis of the lung: A case report

• Published in: Journal of pediatric surgery Vol. 32; no. 12; pp. 1751 - 1753
• Main Authors: Kuga, Takayuki, Esato, Kensuke, Kaneko, Junko, Yamagata, Yoshiaki, Hoshii, Yoshinobu, Takahashi, Mutsuo
• Format: Journal Article
• Language: English
• Published: Philadelphia, PA Elsevier Inc 01-12-1997; Elsevier
• Subjects: Biological and medical sciences; Cystic Adenomatoid Malformation of Lung, Congenital - pathology; Cystic Adenomatoid Malformation of Lung, Congenital - physiopathology; Female; Hematopoiesis, Extramedullary; Humans; Infant, Newborn; Lung - pathology; Medical sciences; Pneumology; Respiratory system : syndromes and miscellaneous diseases; Congenital cystic adenomatoid malformation; extramedulalry hematopoiesis; Human; Lung disease; Radiodiagnosis; Respiratory disease; Lung; Congenital disease; Nuclear magnetic resonance imaging; Case study; Radiography; Pathology; Symptomatology; Histopathology; Newborn; Treatment; Malformation; Surgery; Extramedullary hematopoiesis; Medical imagery; Female; Diagnosis; Lobectomy; Cystic adenomatoid malformation
• ISSN: 0022-3468; 1531-5037
• DOI: 10.1016/S0022-3468(97)90525-X

The authors report a case of congenital cystic adenomatoid malformation of the lung (CCAM) with extramedullary hematopoiesis (EMH). A baby girl suffered from Rh incompatibility and hemolytic anemia. She exhibited respiratory distress. Chest radiography and magnetic resonance imaging findings showed a CCAM. A resection of the upper and middle lobes of the right lung was performed. Histological examination showed a CCAM of Stocker's type II with EMH. EMH in the lung is very rare. The authors speculate that the cause of our case originated from Rh incompatibility and development arrest in the CCAM lung.