Living in the sub-sahara with anhidrotic ectodermal dysplasia: Report of two cases

Ectodermal dysplasia occurs worldwide. It is a hereditary disorder, and there are predominately two forms as follows: X-linked anhidrotic form and an autosomal dominant hidrotic form. It is mainly characterized by defects of the hairs which are sparse, nail defects, dental abnormalities, and the pre...

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Bibliographic Details
Published in:Medical journal of Dr. D Y Patil University Vol. 11; no. 4; pp. 352 - 354
Main Author: Ibrahim Aliyu
Format: Journal Article
Language:English
Published: Wolters Kluwer Medknow Publications 2018
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Summary:Ectodermal dysplasia occurs worldwide. It is a hereditary disorder, and there are predominately two forms as follows: X-linked anhidrotic form and an autosomal dominant hidrotic form. It is mainly characterized by defects of the hairs which are sparse, nail defects, dental abnormalities, and the presence or absence of the eccrine glands. However, our cases had an abnormality of all four ectodermal structures. While they refused dental prosthesis, their major complaint had been heat intolerance which is a big treatment challenge in a hot climate as experienced in Kano Nigeria.
ISSN:2589-8302
2278-7119
DOI:10.4103/MJDRDYPU.MJDRDYPU_213_17