Retinal vasculitis in Susac syndrome: case report

• Published in: Arquivos brasileiros de oftalmologia Vol. 72; no. 3; pp. 397 - 399
• Main Authors: Milbratz, Gherusa Helena, Marquardt, Francisco Azevedo, Guimarães Neto, Heriberto Pinto, Marquardt, Daniel Azevedo, Souza, Eduardo Soares Maia Vieira de
• Format: Journal Article
• Language: English
• Published: Brazil Conselho Brasileiro de Oftalmologia 01-05-2009
• Subjects: Adult; Brain Diseases - diagnosis; Brain Diseases - drug therapy; Headache - etiology; Hearing Loss, Bilateral - etiology; Humans; Male; Nausea - etiology; OPHTHALMOLOGY; Retinal Vasculitis - diagnosis; Retinal Vasculitis - drug therapy; Syndrome; Fluorescein angiography; Vasculite retiniana; Vasculite do sistema nervoso central; Vasculitis, central nervous system; Retinal vasculitis; Perda auditiva neurossensorial; Angiofluoresceinografia; Hearing loss, sensorineural
• ISSN: 0004-2749; 1678-2925; 1678-2925
• DOI: 10.1590/S0004-27492009000300024

A 29 year old male was admitted at the emergency room suffering from gradually worsening headache followed by nausea. In the hospital patient presented with lethargy, reduction of consciousness level and bilateral hypoacusis. Ophthalmic examination and fluorescein angiography showed retinal vasculitis. This finding was crucial to the diagnosis of Susac syndrome, a rare disease characterized by vasculopathy of retina, encephalic tissues and cochlea. Patient was treated with immunosuppressors to prevent him from developing severe sequelae of this disease.