Invasive procedures in the oral cavity of individuals with Bernard–Soulier syndrome: An integrative review

• Published in: Special care in dentistry Vol. 42; no. 3; pp. 281 - 285
• Main Authors: Tieghi Neto, Victor, Viola, Vivian Palata, Júnior, Luiz Alberto Valente Soares, Santos, Paulo Sergio da Silva
• Format: Journal Article
• Language: English
• Published: United States Wiley Subscription Services, Inc 01-05-2022
• Subjects: Bernard-Soulier syndrome; Bernard-Soulier Syndrome - complications; Bernard-Soulier Syndrome - therapy; Bleeding; bleeding disorder; blood coagulation disorders; blood platelet disorders; Case reports; dental care; Humans; inherited coagulation disorders; Literature reviews; Mouth; oral care; Oral cavity; Patients; Thrombocytopenia; blood coagulation disorders; inherited coagulation disorders; bleeding disorder; dental care; oral care; blood platelet disorders; Bernard-Soulier syndrome
• ISSN: 0275-1879; 1754-4505
• DOI: 10.1111/scd.12680

Aim
Bernard–Soulier syndrome (BSS) is an inherited bleeding disorder characterized by macroplatelets and thrombocytopenia, prolonged bleeding time, and a prevalence of less than 1 in 1,000,000. In view of the recognition of the risk of bleeding and the management of daily surgical practice in these patients, adequate strategies are necessary to provide the safest care. This article aims to perform an integrative review of the literature on the management of invasive procedures in the oral cavity of individuals with BSS.
Method
The PubMed/Medline and LILACS databases were searched using Boolean operators related to BSS, bleeding disorders, and oral care.
Results
As a result, only five articles with the main theme were included: one letter to the editor and four case reports, described chronologically as to date of publication, classification of the article, and medical/odontological measures taken.
Conclusion
We conclude with this review the need for adequate knowledge of surgeons regarding coagulation disorders and the need to discuss and plan procedures with the hematology team, as well as the importance of the notion of management of possible complications resulting from invasive treatments in the oral cavity of patients with BSS.