Primary lymphangiectasia of the gastrointestinal tract

• Published in: Terapevtic̆eskii arhiv Vol. 90; no. 3; pp. 96 - 98
• Main Authors: Esedov, E M, Abasova, A S, Akhmedova, F D, Musaeva, L N
• Format: Journal Article
• Language: English; Russian
• Published: Russia (Federation) "Consilium Medicum" Publishing house 19-04-2018
• Subjects: alpha 1-Antitrypsin - analysis; clinical observation; Edema; Gastrointestinal Tract; Humans; hypoproteinemic edema; intestinal lymphangiectasia; Lymphangiectasis, Intestinal - diagnosis; Lymphangiectasis, Intestinal - therapy; medium chain triglycerides; Triglycerides; intestinal lymphangiectasia; hypoproteinemic edema; clinical observation; medium chain triglycerides
• ISSN: 0040-3660; 2309-5342
• DOI: 10.26442/terarkh201890396-98

Intestinal lymphangiectasia is a very rare pathology, characterized by the presence of enlarged lymphatic vessels in all layers of the intestinal wall and in the mesentery. As a result, "lymphatic lakes" are formed, through which lymph exudates into the lumen of the intestine. The main manifestation is hypoproteinemic edema. Diagnosis of the disease is based on laboratory-instrumental methods of investigation, including by determining in the stool α-1 antitrypsin as a screening test. Treatment includes: a diet rich in calcium, trace elements, be sure to use medicinal foods enriched with medium chain triglycerides, substitution and symptomatic therapy.