Large epidural hematoma in a child with progeria syndrome complicated by posterior cerebral artery stroke: A case report

• Published in: Archives of pediatric neurosurgery Vol. 5; no. 2; p. e1872023
• Main Authors: Silva Neto, Angelo, Silva Aires, Felipe Augusto, Torquato Cardoso Lopes, Elisa, Do Vale Beserra, Eric Cymon
• Format: Journal Article
• Language: English
• Published: Brazilian Society for Pediatric Neurosurgery 01-05-2023
• Subjects: epidural hematoma; hutchison-gilford progeria syndrome; traumatic brain injury
• ISSN: 2675-3626; 2675-3626
• DOI: 10.46900/apn.v5i2.187

Hutchinson-Gilford progeria Syndrome (HGPS) is a genetic disease in which patients manifest with a prematurely aged appearance and cardiovascular disease due to atherosclerosis. A 13-year-old male patient with HGPS was admitted with a history of trauma in the right temporoparietal region of the head, evolving with headache, worsening of previous left hemiparesis and right blepharoptosis. Head tomography showed a large epidural hematoma at the right parieto-occiptal convexity. A craniotomy was performed for drainage of the hematoma. After good evolution, the control tomography showed effective drainage of the hematoma with a new ischemia in the right posterior cerebral artery. In this case possibly the syndrome-related cerebrovascular atherosclerosis contributed to the formation of hematoma and postoperative ischemia.