Chest wall reconstruction in Marfan syndrome following aortic root replacement

Chest wall and spine deformities are common in Marfan syndrome, and often coexist with cardiac defects. Surgery is often needed to both the aortic root and the anterior chest wall, and early spinal surgery is not uncommon. We describe a case of severe thoracic cage deformity with aortic root dilatat...

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Bibliographic Details
Published in:	Asian cardiovascular & thoracic annals Vol. 22; no. 7; pp. 872 - 874
Main Authors:	Bezuska, Laurynas, Mussa, Shaffi, Muthialu, Nagarajan
Format:	Journal Article
Language:	English
Published:	London, England SAGE Publications 01-09-2014
Subjects:	Adolescent Aortic Aneurysm - diagnosis Aortic Aneurysm - etiology Aortic Aneurysm - surgery Blood Vessel Prosthesis Implantation Humans Magnetic Resonance Imaging Male Marfan Syndrome - complications Marfan Syndrome - diagnosis Osteotomy Pectus Carinatum - complications Pectus Carinatum - diagnosis Pectus Carinatum - surgery Reconstructive Surgical Procedures Thoracic Surgical Procedures Treatment Outcome Aorta Funnel chest pathologic Dilatation thoracic Marfan syndrome
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Summary:	Chest wall and spine deformities are common in Marfan syndrome, and often coexist with cardiac defects. Surgery is often needed to both the aortic root and the anterior chest wall, and early spinal surgery is not uncommon. We describe a case of severe thoracic cage deformity with aortic root dilatation, which was managed by a staged approach, with a very good final result.
Bibliography:	ObjectType-Case Study-2 SourceType-Scholarly Journals-1 ObjectType-Feature-4 content type line 23 ObjectType-Report-1 ObjectType-Article-3
ISSN:	0218-4923 1816-5370
DOI:	10.1177/0218492313496586