Inflammatory linear verrucous epidermal nevus syndrome

• Published in: Nasza dermatologia online Vol. 6; no. 3; pp. 369 - 371
• Main Authors: Yorulmaz, Ahu, Cakmak, Seray, Hazar Tantoglu, Burcu, Artuz, Ferda, Kadan, Elcin, Sen, Elif
• Format: Journal Article
• Language: English
• Published: Slupsk Our Dermatology Online 01-07-2015
• Subjects: Biopsy; Defects; Dermatology; Inflammatory linear verrucous epidermal nevus syndrome; Intellectual disabilities; Psoriasis
• ISSN: 2081-9390; 2081-9390
• DOI: 10.7241/ourd.20153.101

Upon dermatological examination, we observed multiple erythematous scaly papules coalescing into linear plaques following the lines of Blaschko on the left side of his trunk, medial aspect of his left arm and elbow, also medial aspect of his left leg down to the plantar region (Figs 1-3). Figure 1 [See PDF] Erythematous papules coalescing into linear plaques following the lines of Blaschko Figure 2 [See PDF] Psoriasiform papules and plaques in a Blaschko-linear distribution Figure 3 [See PDF] Blaschkoid papules in a closer view Figure 4 [See PDF] Histopathological findings, (H&Ex40) Prior to the study, patient gave written consent to the examination and biopsy after having been informed about the procedure. Lesions are generally on a limb, most frequently left lower extremity, although rare bilateral and widespread involvements have been described. [...]since CHILD syndrome (congenital hemidysplasia with ichthyosiform erythroderma and limb defects) is characterized by unilateral erythematous verrucous lesions, infrequent reports of limb reduction in association with ILVEN have prompted the idea that ILVEN represents a forme fruste of CHILD syndrome [2,3].