Difficult diagnostics of a rare cause of pulmonary hypertension: a case report

• Published in: Rossiĭskiĭ kardiologicheskiĭ zhurnal Vol. 26; no. 1S; p. 4209
• Main Authors: Kizhvatova, N. V., Kosmacheva, E. D., Kruchinova, S. V., Namitokov, A. M.
• Format: Journal Article
• Language: English; Russian
• Published: FIRMA «SILICEA» LLC 22-04-2021
• Subjects: pulmonary hypertension; sezary syndrome; t-cell lymphoma
• ISSN: 1560-4071; 2618-7620
• DOI: 10.15829/1560-4071-2021-4209

Pulmonary hypertension is a syndrome difficult for differential diagnosis, which is the outcome of various pathological conditions. With the exclusion of the most common causes of pulmonary hypertension (left heart disorders and pulmonary embolism), further search for cause often becomes an insoluble problem. Sezary syndrome is classified as a rare type of cutaneous T-cell lymphomas. Early diagnosis of this syndrome is important for the initiation of adequate therapy, since cases of complete recovery or long-term remission in patients with Sezary syndrome are very rare. A case report of Sezary syndrome verification in cardiology practice is described.