Bilateral macular staphylomas in a patient with cone dystrophy

• Published in: British journal of ophthalmology Vol. 87; no. 8; pp. 1049 - 1051
• Main Authors: Apte, R S, Sunness, J S, Goldstein, B G, Park, W L, Raden, R Z, Elman, M J
• Format: Journal Article
• Language: English
• Published: BMA House, Tavistock Square, London, WC1H 9JR BMJ Publishing Group Ltd 01-08-2003; BMJ Publishing Group LTD; Copyright 2003 British Journal of Ophthalmology
• Subjects: Adult; Care and treatment; Case studies; cone dystrophy; Female; Humans; Letters; Macular degeneration; Macular Degeneration - complications; macular staphylomas; Myopia; Retina; Scleral Diseases - complications; Scotoma - etiology; Ultrasonic imaging; Vision disorders; Visual Fields; Maryland
• ISSN: 0007-1161; 1468-2079
• DOI: 10.1136/bjo.87.8.1049-a

A posterior staphyloma is characterised by scleral ectasia and is pathognomonic for pathological myopia. 1, 2 Posterior staphylomas are classified in to five types based on the anatomic location. 1 Type 1 staphylomas extend from the nasal border of the optic nerve into the macular region and are the most frequent staphyloma seen in myopes. 1 Type 2 staphylomas are centred on the macula while type 3 staphylomas are centred on the optic disc without macular extension. 1 Type 4 staphylomas are located nasal to the optic disc and type 5 staphylomas develop inferior to the optic disc. 1 Staphylomas can be associated with multiple complications including retinal pigment epithelial atrophy, lacquer cracks, retinal and subretinal haemorrhages, and choroidal neovascularisation. 1, 3 This report describes a patient with undiagnosed, bilateral type 2 macular staphylomas compounded by cone dystrophy. Given the significant association of macular staphylomas with numerous complications listed above, especially the risk for choroidal neovascularisation and haemorrhage, such patients should receive counselling regarding its symptoms and receive periodic comprehensive ophthalmological examinations.