Functioning metastatic paraganglioma of the urinary bladder in a 10-year-old child

• Published in: BMJ case reports Vol. 2017; p. bcr-2017-220533
• Main Authors: El Alayli, Alaeddine, El Amine, Mohammad Ali, El Hout, Yaser, Naffaa, Lena
• Format: Journal Article
• Language: English
• Published: England BMJ Publishing Group LTD 19-07-2017; BMJ Publishing Group
• Series: Case Report
• Subjects: Accuracy; Biopsy; Bladder cancer; Case reports; Child; Cystectomy; Dopamine; Gangrene; Humans; Lymphatic system; Magnetic Resonance Imaging; Male; Medical imaging; Metastasis; Middle East; Mutation; Neoplasm Metastasis; Neuroendocrine tumors; Paraganglioma - diagnostic imaging; Paraganglioma - surgery; Pathology; Plasma; Rare Disease; Tomography; Treatment Outcome; Tumors; Ultrasonic imaging; Ultrasonography; Urinary Bladder Neoplasms - diagnostic imaging; Urinary Bladder Neoplasms - surgery; Urine; Urological cancer; Radiology; Cancer intervention; Urological cancer; Urological surgery; Neuroendocrinology
• ISSN: 1757-790X; 1757-790X
• DOI: 10.1136/bcr-2017-220533

Paragangliomas of the urinary bladder are very rare tumours representing less than 1% of bladder tumours. Preoperative diagnosis is essential to avoid perioperative complications related to catecholamine release. A high index of suspicion should be maintained when the classical symptoms of voiding-related paroxysms of headache, palpitation and dizziness are present. We present a rare case of malignant paraganglioma of the urinary bladder in a 10-year-old boy. The patient had the classic presentation. We review the radiological diagnostic tools and findings of this rare entity.