Giant fibromyxoid tumors of the adventitial dermis. Forme fruste of trichodiscoma?

A 36-year-old paraplegic man developed multiple giant fibromyxoid tumors surrounding a meningomyelocele scar that we believe are forme fruste of trichodiscomas. Histologic examination showed a papillated, slightly hyperplastic epidermis surrounding a delicate fibrovascular proliferation set in a str...

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Bibliographic Details
Published in:	The American journal of dermatopathology Vol. 13; no. 4; p. 403
Main Authors:	McCalmont, C S, White, W L, Jorizzo, J L
Format:	Journal Article
Language:	English
Published:	United States 01-08-1991
Subjects:	Adult Cicatrix - complications Fibroma - complications Fibroma - pathology Humans Male Meningomyelocele - surgery Neoplasms, Multiple Primary - complications Neoplasms, Multiple Primary - pathology Skin Neoplasms - complications Skin Neoplasms - pathology
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Summary:	A 36-year-old paraplegic man developed multiple giant fibromyxoid tumors surrounding a meningomyelocele scar that we believe are forme fruste of trichodiscomas. Histologic examination showed a papillated, slightly hyperplastic epidermis surrounding a delicate fibrovascular proliferation set in a stroma of loose fibrillar connective tissue and stellate fibroblasts. A melanocytic nevus was incorporated into one of the lesions. We believe that these giant lesions are connective tissue nevi of the adventitial dermis that comprise a new clinical variant of trichodiscoma. The potential significance of the relationship between these abortive trichodiscomas and abnormalities of the neural crest is discussed.
ISSN:	0193-1091
DOI:	10.1097/00000372-199108000-00012