Nutritional aspects of children and adolescents with epidermolysis bullosa: literature review

• Published in: Anais brasileiros de dermatología Vol. 90; no. 2; pp. 217 - 223
• Main Authors: Zidorio, Ana Paula Caio, Dutra, Eliane Said, Leão, Dryelle Oliveira Dias, Costa, Izelda Maria Carvalho
• Format: Journal Article
• Language: English
• Published: Brazil Sociedade Brasileira de Dermatologia 01-04-2015
• Subjects: Adolescent; Adolescent Development; Adolescent nutrition; Child; Child Development; Child nutrition; DERMATOLOGY; Energy Intake; Epidermolysis bullosa; Epidermolysis Bullosa - diet therapy; Epidermolysis Bullosa - metabolism; Epidermolysis Bullosa Dystrophica - diet therapy; Epidermolysis Bullosa Dystrophica - metabolism; Humans; Nutritional Requirements - physiology; Nutritional Status - physiology; Review; Child nutrition; Epidermolysis bullosa; Adolescent nutrition
• ISSN: 0365-0596; 1806-4841; 1806-4841; 0365-0596
• DOI: 10.1590/abd1806-4841.20153206

Epidermolysis Bullosa is a genetic disorder that affects mainly the skin, however, all others systems are influenced. The nutritional care of children and adolescents with Epidermolysis Bullosa is a key treatment strategy, since the energy needs are increased due to the disease's metabolism, burdening the immune system and cicatrization process, symptoms caused by the disease hinder the intake and adequate absorption of nutrients, which may result in inadequate growth and development. Because this is a rare disease, there are few professionals who know the characteristics of both the clinical evolution and nutritional and dietary treatments. This literature review discusses the latest knowledge on energy and specific nutrient requirements to the dietary treatment and monitoring of children and adolescents with Epidermolysis Bullosa.