Granulomatosis with polyangiitis, a new nomenclature for Wegener's Granulomatosis--Case report

• Published in: Anais brasileiros de dermatología Vol. 90; no. 3 Suppl 1; pp. 101 - 103
• Main Authors: Lima, Alexandre Moretti de, Torraca, Pedro de Freitas Silva, Rocha, Sheila Pereira da, Santiago, Carmelia Matos Reis, Ferraz, Fabio Humberto Ribeiro Paes
• Format: Journal Article
• Language: English
• Published: Brazil Sociedade Brasileira de Dermatologia 01-06-2015
• Subjects: Adolescent; Adrenal Cortex Hormones - administration & dosage; Anti-neutrophil cytoplasmic antibody-associated vasculitis; Case Report; DERMATOLOGY; Facial Dermatoses - drug therapy; Facial Dermatoses - pathology; Female; Granulomatosis with Polyangiitis; Granulomatosis with Polyangiitis - drug therapy; Granulomatosis with Polyangiitis - pathology; Humans; Leg Dermatoses - drug therapy; Leg Dermatoses - pathology; Necrosis - pathology; Skin Ulcer - drug therapy; Skin Ulcer - pathology; Terminology as Topic; Vasculitis; Anti-neutrophil cytoplasmic antibody-associated vasculitis; Granulomatosis with Polyangiitis; Vasculitis
• ISSN: 0365-0596; 1806-4841; 1806-4841; 0365-0596
• DOI: 10.1590/abd1806-4841.20153455

The granulomatosis with polyangiitis, initially known as Wegener's granulomatosis, is a small and medium vessels vasculitis. It's classic form presents a triad: necrotizing granuloma of respiratory tract, necrotizing cutaneous vasculitis and glomerulonephritis. This vasculitis has cytoplasmic antineutrophil antibodies as signal. This work illustrates a case, of multisystemic rare disease, in which the segment and treatment were considered satisfactory for symptoms remission.