Fetal Noncompaction Cardiomyopathy and Histologic Diagnosis of Spongy Myocardium: Case Report and Review of the Literature

• Published in: Revista Brasileira de ginecologia e obstetrícia Vol. 40; no. 11; pp. 722 - 725
• Main Authors: Nappi, Luigi, Vasciaveo, Lorenzo, Sorrentino, Felice, Scutiero, Gennaro, Iannone, Piergiorgio, Greco, Pantaleo
• Format: Journal Article
• Language: English
• Published: Brazil Thieme Revinter Publicações Ltda 01-11-2018; Federação Brasileira das Sociedades de Ginecologia e Obstetrícia
• Subjects: Case Report; Female; Heart - diagnostic imaging; Humans; Isolated Noncompaction of the Ventricular Myocardium - diagnostic imaging; left ventricular noncompaction cardiomyopathy; Myocardium - pathology; noncompaction cardiomyopathy; OBSTETRICS & GYNECOLOGY; spongy myocardium; Ultrasonography, Prenatal; Young Adult; left ventricular noncompaction cardiomyopathy; spongy myocardium; noncompaction cardiomyopathy
• ISSN: 0100-7203; 1806-9339; 1806-9339
• DOI: 10.1055/s-0038-1673677

Noncompaction cardiomyopathy (NCCM) and left ventricular noncompaction (LVNC), in their isolated form, are rare cardiomyopathies. They are characterized by a thickened myocardium due to the presence of deep trabeculae recesses, and to thick trabeculae. This condition is associated with a variable clinical phenotype including heart failure, thromboembolism, and sudden death. We report a case of LVNC at 26 weeks and 4 days of gestation revised on the basis of what is currently reported in the literature. A review of the literature was performed to better describe this rare condition. Left ventricular noncompaction is a rare fetal condition and it should be suspected in case of cardiomyopathy.