Revised diagnostic criteria for the pseudotumor cerebri syndrome in adults and children

• Published in: Neurology Vol. 81; no. 13; pp. 1159 - 1165
• Main Authors: Friedman, Deborah I., Liu, Grant T., Digre, Kathleen B.
• Format: Journal Article
• Language: English
• Published: Hagerstown, MD American Academy of Neurology 24-09-2013; Lippincott Williams & Wilkins
• Subjects: Adolescent; Adult; Age Factors; Biological and medical sciences; Brain - pathology; Diagnosis, Differential; Female; Humans; Intracranial Pressure; Male; Malformations of the nervous system; Medical sciences; Neuroimaging - methods; Neurology; Pseudotumor Cerebri - diagnosis; Reference Values; Spinal Puncture - methods; Spinal Puncture - standards; Human; Nervous system diseases; Central nervous system disease; Benign intracranial hypertension; Diagnosis; Child; Cerebral disorder
• ISSN: 0028-3878; 1526-632X
• DOI: 10.1212/WNL.0b013e3182a55f17

The pseudotumor cerebri syndrome (PTCS) may be primary (idiopathic intracranial hypertension) or arise from an identifiable secondary cause. Characterization of typical neuroimaging abnormalities, clarification of normal opening pressure in children, and features distinguishing the syndrome of intracranial hypertension without papilledema from intracranial hypertension with papilledema have furthered our understanding of this disorder. We propose updated diagnostic criteria for PTCS to incorporate advances and insights into the disorder realized over the past 10 years.