Vertebral Artery Dissection in a Patient With Wildervanck Syndrome

• Published in: Pediatric neurology Vol. 39; no. 3; pp. 218 - 220
• Main Authors: Dirik, Eray, MD, Yiş, Uluç, MD, Dirik, Mehmet Alp, MD, Çakmakçı, Handan, MD, Men, Süleyman, MD
• Format: Journal Article
• Language: English
• Published: New York, NY Elsevier Inc 01-09-2008; Elsevier
• Subjects: Abnormalities, Multiple - pathology; Abnormalities, Multiple - physiopathology; Adolescent; Biological and medical sciences; Ear, Inner - abnormalities; Eye Abnormalities; Female; Hearing Loss, Conductive - pathology; Humans; Klippel-Feil Syndrome - pathology; Klippel-Feil Syndrome - physiopathology; Magnetic Resonance Angiography; Medical sciences; Neck Muscles - abnormalities; Neurology; Pediatrics; Spine - abnormalities; Syndrome; Vascular diseases and vascular malformations of the nervous system; Vertebral Artery Dissection - diagnosis; Vertebral Artery Dissection - physiopathology; Arterial disease; Vascular disease; Dissecting aneurysm; Human; Nervous system diseases; Vertebral artery; Cardiovascular disease; Artery dissection
• ISSN: 0887-8994; 1873-5150
• DOI: 10.1016/j.pediatrneurol.2008.06.005

Vertebral artery dissection as a cause of stroke is rarely reported in children. The association between vertebral artery dissection and Klippel-Feil syndrome is also very rare. We report on a case of vertebral artery dissection with posterior circulation involvement in a child with Klippel-Feil syndrome after a hard physical-training lesson. She was also diagnosed with Wildervanck syndrome, with additional clinical findings. Vertebral artery dissection should be considered in patients with Klippel-Feil syndrome who present with acute-onset neurologic signs. Movements such as hyperextension with rotation of the neck should be avoided in these cases.