Emergent presentation of Langerhans cell histiocytosis in a pediatric patient: Acute cerebellar involvement causing obstructive hydrocephalus requiring posterior fossa decompression

• Published in: The Indian journal of radiology & imaging Vol. 27; no. 4; pp. 432 - 435
• Main Authors: Rajderkar, Dhanashree A, Shah, Mrunal L, Shah, Jehan L
• Format: Journal Article
• Language: English
• Published: A-12, Second Floor, Sector -2, NOIDA -201301, India Thieme Medical and Scientific Publishers Private Ltd 01-10-2017; Medknow Publications and Media Pvt. Ltd; Georg Thieme Verlag Stuttgart; Medknow Publications & Media Pvt Ltd; Thieme Medical and Scientific Publishers Pvt. Ltd
• Subjects: Autoimmune diseases; Care and treatment; Case studies; Complications and side effects; Diagnosis; Diagnostic imaging; emergent decompression; Histiocytosis; intracranial langerhans cell histiocytosis; obstructive hydrocephalus; Paediatric; India; obstructive hydrocephalus; intracranial Langerhans cell histiocytosis; Emergent decompression
• ISSN: 0971-3026; 0970-2016; 1998-3808
• DOI: 10.4103/ijri.IJRI_389_16

Abstract
Langerhans cell histiocytosis (LCH) is a disorder of the monocyte-macrophage system that can be unifocal or systemic. Here, we present a pediatric case who initially presented with osseous LCH but again presented 6 years later emergently with cerebellar symptoms, cerebellar mass and obstructive hydrocephalus. Patient underwent biopsy of the cerebellum which was path proven intracranial LCH.