A circumflex coronary artery-to-right atrial fistula in a 10-month-old child

• Published in: Cardiovascular Journal of Africa Vol. 27; no. 6; pp. e1 - e3
• Main Authors: Şişli, Emrah, Ayik, Mehmet Fatih, Akyüz, Muhammet, Dereli, Münevver, Atay, Yüksel
• Format: Journal Article
• Language: English
• Published: South Africa Clinics Cardive Publishing 23-12-2016
• Subjects: Abnormalities, Multiple; Cardiac Surgical Procedures; Case Report; Coronary Vessel Anomalies - diagnostic imaging; Coronary Vessel Anomalies - surgery; Echocardiography, Doppler, Color; Heart Atria - abnormalities; Heart Atria - diagnostic imaging; Heart Atria - surgery; Heart Septal Defects, Atrial - diagnostic imaging; Heart Septal Defects, Atrial - surgery; Humans; Incidental Findings; Infant; Male; Treatment Outcome; Vascular Fistula - diagnostic imaging; Vascular Fistula - surgery
• ISSN: 1995-1892; 1680-0745
• DOI: 10.5830/CVJA-2016-044

A coronary fistula (CF) is a rare congenital cardiac anomaly in which there is a connection between the coronary artery and a cardiac chamber or a great vessel. In the paediatric population, a CF is usually asymptomatic. While the circumflex coronary artery (Cx) is the least common source of a CF, the right heart chambers are the most common location of drainage. Herein, we present a symptomatic 10-month-old boy with an atrial septal defect (ASD) in whom we incidentally detected a CF, which stemmed from the Cx and drained to the right atrium. Because the patient was symptomatic and his small size was not appropriate for percutaneous closure of the ASD, surgical closure of the ASD and CF was performed.