PRIMARY RHABDOMYOSARCOMA OF THE LUNG ARISING OVER CYSTIC PULMONARY ADENOMATOID MALFORMATION

• Published in: Pediatric hematology and oncology Vol. 22; no. 6; pp. 525 - 529
• Main Authors: Doladzas, Theodoros, Arvelakis, Antonios, Karavokyros, I. G., Gougoudi, Evagelia, Pikoulis, Emmanouil, Patsouris, Efstratios, Michail, P. O.
• Format: Journal Article
• Language: English
• Published: England Informa UK Ltd 01-09-2005; Taylor & Francis
• Subjects: Child, Preschool; congenital lung malformation; Cystic Adenomatoid Malformation of Lung, Congenital - complications; Cystic Adenomatoid Malformation of Lung, Congenital - pathology; Cystic Adenomatoid Malformation of Lung, Congenital - therapy; Disease-Free Survival; Female; Humans; lung cysts; Lung Neoplasms - complications; Lung Neoplasms - pathology; Lung Neoplasms - therapy; pulmonary rhabdomyosarcoma; Rhabdomyosarcoma - complications; Rhabdomyosarcoma - pathology; Rhabdomyosarcoma - therapy
• ISSN: 0888-0018; 1521-0669
• DOI: 10.1080/08880010591002396

The authors report the case of a 2-year-old girl with pulmonary cystic adenomatoid malformation type II who presented with a mass on the lower lobe of the left lung. Resection and histological examination revealed pleomorphic rhabdomyosarcoma. Chemotherapy and radiotherapy followed the operation and the girl is alive and in perfect condition 10 years after the operation. The literature on primary rhabdomyosarcoma of the lung in children is reviewed.