Angiofibromatoid histiosarcoma of the pulmonary artery
Abstract We describe the surgical management of a rare pulmonary angiomatoid fibrous histiosarcoma (AFH). A 62-year-old lady presented with shortness of breath and found to have a large left main pulmonary artery defect that was positron emission tomography-avid. Following discussion in a thoracic m...
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| Published in: | Journal of surgical case reports Vol. 2021; no. 4; p. rjab132 |
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| Main Authors: | , , |
| Format: | Journal Article |
| Language: | English |
| Published: |
England
Oxford University Press
01-04-2021
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| Subjects: | |
| Online Access: | Get full text |
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| Summary: | Abstract
We describe the surgical management of a rare pulmonary angiomatoid fibrous histiosarcoma (AFH). A 62-year-old lady presented with shortness of breath and found to have a large left main pulmonary artery defect that was positron emission tomography-avid.
Following discussion in a thoracic multidisciplinary team meeting it was deemed unsafe to biopsy considering its intravascular position. The patient proceeded to theatre for a left pneumonectomy. She was successfully discharged home by Day 7. On follow-up the patient is well, and free of malignancy.
AFH is an incredibly rare form of sarcoma, and in particular in the thoracic region. We have demonstrated successful oncological resection of a rare intravascular lesion in the pulmonary artery. |
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| ISSN: | 2042-8812 2042-8812 |
| DOI: | 10.1093/jscr/rjab132 |