Association of idiopathic retroperitoneal fibrosis, rapidly progressive glomerulonephritis and antiproteinase 3 antineutrophil cytoplasmic antibodies (anti PR3-ANCA)

Association of idiopathic retroperitoneal fibrosis, rapidly progressive glomerulonephritis and antiproteinase 3 antineutrophil cytoplasmic antibodies (anti PR3-ANCA)

We report a case of idiopathic retroperitoneal fibrosis and rapidly progressive glomerulonephritis with serum antiproteinase 3 antineutrophil cytoplasmic antibodies (anti-PR3-ANCA), without clinical or histological signs of Wegener's granulomatosis, in a 46-year-old man. Our case and previously...

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Bibliographic Details
Published in:Clinical nephrology Vol. 70; no. 3; p. 251
Main Authors: Martínez-Odriozola, P, Gutiérrez-Macías, A, Moina Eguren, I, Arrieta Lezama, J
Format: Journal Article
Language:English
Published: Germany 01-09-2008
Subjects:
Antibodies, Antineutrophil Cytoplasmic - blood
Glomerulonephritis - complications
Glomerulonephritis - immunology
Humans
Male
Middle Aged
Myeloblastin - immunology
Retroperitoneal Fibrosis - complications
Retroperitoneal Fibrosis - immunology
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Summary:We report a case of idiopathic retroperitoneal fibrosis and rapidly progressive glomerulonephritis with serum antiproteinase 3 antineutrophil cytoplasmic antibodies (anti-PR3-ANCA), without clinical or histological signs of Wegener's granulomatosis, in a 46-year-old man. Our case and previously reported cases showing the same association support the hypothesis that the association is not fortuitous, but reflects a common immunological mechanism.
ISSN:0301-0430
DOI:10.5414/cnp70251