Upper thoracic extralobar pulmonary sequestration with anomalous blood supply from the subclavian artery

• Published in: Journal of pediatric surgery Vol. 38; no. 4; pp. 626 - 628
• Main Authors: Ito, Fujio, Asaoka, Mineo, Nagai, Noriko, Hayakawa, Fumio
• Format: Journal Article
• Language: English
• Published: Philadelphia, PA Elsevier Inc 01-04-2003; Elsevier
• Subjects: Biological and medical sciences; Bronchopulmonary Sequestration - complications; Bronchopulmonary Sequestration - diagnosis; Bronchopulmonary Sequestration - pathology; Bronchopulmonary Sequestration - surgery; Cystic Adenomatoid Malformation of Lung, Congenital - diagnosis; Diagnosis, Differential; Extralobar pulmonary sequestration; Humans; Infant, Low Birth Weight; Infant, Newborn; Infant, Premature; Investigative techniques, diagnostic techniques (general aspects); Lung - blood supply; Magnetic Resonance Imaging; Male; Medical sciences; Pneumology; Pneumonectomy - methods; Radiodiagnosis. Nmr imagery. Nmr spectrometry; Respiratory Distress Syndrome, Newborn - etiology; Respiratory system; Respiratory system : syndromes and miscellaneous diseases; subclavian artery; Subclavian Artery - abnormalities; Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases; Surgery of the respiratory system; Tomography, X-Ray Computed; Extralobar pulmonary sequestration; subclavian artery; Human; Vascular disease; Case study; Lung disease; Newborn; Respiratory disease; Malformation; Cardiovascular disease; Subclavian artery
• ISSN: 0022-3468; 1531-5037
• DOI: 10.1053/jpsu.2003.50138

The authors report on a newborn boy with extralobar pulmonary sequestration in the right upper thoracic region. Preoperative angiography showed an anomalous large vessel from the right Subclavian artery, supplying the sequestrated lobe. Right thoracotomy was performed to resect the sequestrated lobe, which was diagnosed as extralobar form. This is an extremely rare case of extralobar pulmonary sequestration in which anomalous blood supply from the subclavian artery was seen preoperatively on radiographs. The authors recommend angiographic examination, particularly in case of diagnostic difficulty.