Case Report: A Rare Case of a Ventricular Perivascular Epithelioid Cell Tumor With Histologic Characteristics That Resembled a Primary Cardiac Rhabdomyoma

We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-...

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Bibliographic Details
Published in:	Frontiers in cardiovascular medicine Vol. 8
Main Authors:	Cossío-Aranda, Jorge, Aranda-Frausto, Alberto, Berarducci, Joaquin, Espinola-Zavaleta, Nilda, González-Melchor, Laila, Vázquez-Antona, Clara, Meléndez-Ramirez, Gabriela, Armenta-Moreno, Javier Ivan, Keirns, Candace
Format:	Journal Article
Language:	English
Published:	Frontiers Media S.A 25-10-2021
Subjects:	arrhythmia cardiac tumor cardiooncology Cardiovascular Medicine PEComa perivascular epithelioid cell neoplasm rhabdomyoma of heart
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Summary:	We present the case of a young male patient with an initial diagnosis of a rhabdomyoma that was surgically treated at a different hospital when he was 17. After a 2-year disease-free period, the patient presented another intra-cardiac mass. He refused surgical treatment and died 5 years later. Post-mortem immunochemistry studies of both tumors led to the diagnosis of a primary malignant cardiac PEComa with histopathologic characteristics that resembled a rhabdomyoma with abundant “spider cells.”
Bibliography:	Reviewed by: Ariane Vieira Scarlatelli Macedo, Santa Casa of Sào Paulo, Brazil; Maria Sol Andres, Royal Brompton Hospital, United Kingdom This article was submitted to Cardio-Oncology, a section of the journal Frontiers in Cardiovascular Medicine Edited by: Reto Asmis, Wake Forest School of Medicine, United States
ISSN:	2297-055X 2297-055X
DOI:	10.3389/fcvm.2021.709328