Orthotopic liver transplantation in glucose-6-phosphatase deficiency--Von Gierke disease--with multiple hepatic adenomas and concomitant focal nodular hyperplasia

Von Gierke disease is occasionally complicated by hepatic adenomas (HAs) causing great concern owing to the current difficulties in monitoring them regarding malignant transformation. Orthotopic liver transplantation (OLT) is proposed as a therapeutic tool when multiple HAs and poor metabolic contro...

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Bibliographic Details
Published in:	Journal of pediatric endocrinology & metabolism : JPEM Vol. 20; no. 4; p. 545
Main Authors:	Carreiro, Gerson, Villela-Nogueira, Cristiane A, Coelho, Henri ue Sérgio M, Basto, Samanta, Pannain, Vera Lucia, Caroli-Bottino, Adriana, Ribeiro Filho, Joaquim
Format:	Journal Article
Language:	English
Published:	Germany 01-04-2007
Subjects:	Adenoma - complications Adenoma - diagnosis Adenoma - therapy Adult Female Focal Nodular Hyperplasia - complications Focal Nodular Hyperplasia - diagnosis Focal Nodular Hyperplasia - therapy Glycogen Storage Disease Type I - complications Glycogen Storage Disease Type I - diagnosis Glycogen Storage Disease Type I - therapy Humans Liver Neoplasms - complications Liver Neoplasms - diagnosis Liver Neoplasms - therapy Liver Transplantation Prognosis Transplantation, Homologous Treatment Outcome
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