Torsion of a Hydrosalpinx in a Virgin Patient with Mayer-Rokitansky-Küster-Hauser Syndrome: Report of a Rare Condition and Its Possible Etiology

• Published in: Journal of pediatric & adolescent gynecology Vol. 26; no. 2; pp. e37 - e38
• Main Authors: Kondo, Eiji, MD, PhD, Tabata, Tsutomu, MD, PhD, Shiozaki, Takaya, MD, Motohashi, Takashi, MD, Tanida, Koji, MD, Okugawa, Toshiharu, MD, PhD, Ikeda, Tomoaki, MD, PhD
• Format: Journal Article
• Language: English
• Published: United States Elsevier Inc 01-04-2013
• Subjects: 46, XX Disorders of Sex Development; Abdominal Pain - etiology; Abnormalities, Multiple; Adult; Chlamydia Infections - etiology; Chlamydia trachomatis; Congenital Abnormalities; E-cadherin; Female; Humans; Hydrosalpinx; Kidney - abnormalities; Laparoscopy; Magnetic Resonance Imaging; Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome; Mullerian Ducts - abnormalities; Obstetrics and Gynecology; Pediatrics; Salpingectomy; Salpingitis - diagnosis; Salpingitis - etiology; Salpingitis - surgery; Sexual Abstinence; Somites - abnormalities; Spine - abnormalities; Torsion; Torsion Abnormality - diagnosis; Torsion Abnormality - etiology; Torsion Abnormality - surgery; Ultrasonography; Uterus - abnormalities; Vagina - abnormalities; Laparoscopy; Hydrosalpinx; Torsion; E-cadherin; Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome
• ISSN: 1083-3188; 1873-4332
• DOI: 10.1016/j.jpag.2012.11.006

Abstract Background To describe a rare case of hydrosalpinx torsion in a virgin patient with Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome. Case A 25-year-old woman with previously diagnosed MRKH syndrome in whom lower abdominal pain led to discovery and resection of a hydosalpinx of unusual origin in a university hospital department of obstetrics and gynecology, Japan. Results and Conclusions Laparoscopy revealed a twisted left-sided hydrosalpinx, and the mass was resected laparoscopically. Results of the blood test for Chlamydia trachomatis were positive, but results of the PCR test were negative. Our case was unusual in that hydrosalpinx is rare in virgin patients with MRKH. The cause of the hydrosalpinx was unclear, but one possibility is excess tubal secretions from the fallopian tube.