Alveolar hemorrhage with epithelioid hemangioendothelioma. A previously unreported manifestation of a rare tumor

• Published in: The American review of respiratory disease Vol. 142; no. 3; p. 700
• Main Authors: Carter, E J, Bradburne, R M, Jhung, J W, Ettensohn, D B
• Format: Journal Article
• Language: English
• Published: United States 01-09-1990
• Subjects: Aged; Hemangioendothelioma - complications; Hemangioendothelioma - diagnostic imaging; Hemangioendothelioma - pathology; Hemoptysis - etiology; Humans; Lung - diagnostic imaging; Lung - pathology; Lung Neoplasms - complications; Lung Neoplasms - diagnostic imaging; Lung Neoplasms - pathology; Male; Radiography
• ISSN: 0003-0805
• DOI: 10.1164/ajrccm/142.3.700

Epithelial hemangioendothelioma (EH), originally termed intravascular sclerosing bronchioloalveolar tumor (IVBAT), is a rare pulmonary vascular neoplasm usually associated with an indolent but slowly progressive clinical course. We describe a patient with EH who presented with alveolar hemorrhage and died within 8 wk. This report extends the clinical spectrum of epithelial hemangioendothelioma to include this aggressive form. EH should be considered in the differential diagnosis of alveolar hemorrhage syndrome.