Kaposiform hemangioendothelioma with overlapping features of rapidly involuting congenital hemangioma and a delayed complication of necrotizing fasciitis

• Published in: Pediatric dermatology Vol. 37; no. 5; pp. 902 - 906
• Main Authors: Belmesk, Lina, Dubois, Josée, Caouette‐Laberge, Louise, David, Michèle, Bortoluzzi, Patricia, Kokta, Victor, Hatami, Afshin, McCuaig, Catherine C.
• Format: Journal Article
• Language: English
• Published: United States Wiley Subscription Services, Inc 01-09-2020
• Subjects: Atrophy; Case reports; Child, Preschool; coagulopathy; Fasciitis; Fasciitis, Necrotizing - diagnosis; Fasciitis, Necrotizing - etiology; Forearm; Hemangioendothelioma; Hemangioma; Humans; Kaposiform Hemangioendothelioma; Kasabach-Merritt Syndrome; Male; Necrotizing fasciitis; Pediatrics; rapidly involuting congenital hemangioma; Sarcoma; Sarcoma, Kaposi; Septic shock; Skin Neoplasms; Thrombophlebitis; vascular tumor; Vein & artery diseases; vascular tumor; Hemangioma; rapidly involuting congenital hemangioma; coagulopathy; Kaposiform Hemangioendothelioma
• ISSN: 0736-8046; 1525-1470
• DOI: 10.1111/pde.14262

We report the case of a male infant born at term with kaposiform hemangioendothelioma (KHE) of the right forearm and coagulopathy. Our case was unusual as it involuted leaving subcutaneous atrophy and prominent veins, which are more commonly observed in rapidly involuting congenital hemangioma. At 3 years of age, the child developed recurrent superficial thrombophlebitis localized to the area where the KHE had regressed. Subsequently, he developed necrotizing fasciitis and thrombotic veins in the same location and group A streptococcal septic shock.