Total anomalous systemic and pulmonary venous connection

• Published in: Asian cardiovascular & thoracic annals Vol. 23; no. 1; pp. 61 - 63
• Main Authors: Mishra, Amit, Sharma, Pranav, Shah, Ritesh, Oswal, Nilesh, Rana, Yashpal
• Format: Journal Article
• Language: English
• Published: London, England SAGE Publications 01-01-2015
• Subjects: Abnormalities, Multiple; Arterial Pressure; Cardiac Surgical Procedures; Heart Defects, Congenital - diagnosis; Heart Defects, Congenital - physiopathology; Heart Defects, Congenital - surgery; Heart Septal Defects, Atrial - diagnosis; Heart Septal Defects, Atrial - physiopathology; Heart Septal Defects, Atrial - surgery; Humans; Infant; Male; Pulmonary Circulation; Pulmonary Veins - abnormalities; Pulmonary Veins - physiopathology; Pulmonary Veins - surgery; Tomography, X-Ray Computed; Treatment Outcome; Vena Cava, Inferior - abnormalities; Vena Cava, Inferior - physiopathology; Vena Cava, Inferior - surgery; Vena Cava, Superior - abnormalities; Vena Cava, Superior - physiopathology; Vena Cava, Superior - surgery; Atrial septal defect; Congenital heart defect; Pulmonary veins; Superior vena cava; Inferior vena cava
• ISSN: 0218-4923; 1816-5370
• DOI: 10.1177/0218492313495859

Total anomalous systemic and pulmonary venous connection is an extremely rare congenital cardiac anomaly. We present our unique experience of managing this complex partially diagnosed cardiac anomaly in a 16-month-old boy. The systemic venous anomaly was not detected during the initial preoperative evaluation. He was doing well on follow-up, with normal pulmonary artery pressure.