Thymic Carcinoid Associated With Multiple Endocrine Neoplasia Syndrome Type I

• Published in: Archivos de bronconeumología (English ed.) Vol. 49; no. 3; pp. 122 - 125
• Main Authors: Recuero Díaz, José Luis, Embún Flor, Raúl, Menal Muñoz, Patricia, Hernández Ferrández, Jorge, Arrarás Martínez, Miguel Jesús, Rivas de Andrés, Juan José
• Format: Journal Article
• Language: English
• Published: Spain Elsevier España 01-03-2013
• Subjects: Adult; Carcinoid Tumor - diagnosis; Carcinoide tímico; Humans; Internal Medicine; Male; Multiple Endocrine Neoplasia Type 1; Multiple endocrine neoplasia type I; Neoplasia endocrina múltiple tipo I; Neoplasms, Multiple Primary - diagnosis; Pulmonary/Respiratory; Thymectomy; Thymic carcinoid; Thymus Neoplasms - diagnosis; Timectomía; Carcinoide tímico; Neoplasia endocrina múltiple tipo I; Multiple endocrine neoplasia type I; Thymectomy; Thymic carcinoid; Timectomía
• ISSN: 1579-2129; 1579-2129
• DOI: 10.1016/j.arbr.2013.01.008

Abstract Thymic carcinoids are a rare entity that may be associated with endocrine diseases like Cushing's syndrome or multiple endocrine neoplasia syndrome type I (MEN1). These tumors represent 4% of anterior mediastinal tumors and are characterized by their very aggressive behavior. We present the case of a patient with a previous MEN 1 diagnosis in whom, during the follow up of his disease, a thoracic image compatible with thymic carcinoid was detected. After an extended thymectomy that included peri-thymic fat resection, the clinical diagnosis was confirmed. A follow-up examination 14 months later revealed a suspicious lesion that suggested local recurrence, therefore the patient was reoperated on. The pathology report of this surgery indicated post-radiation fibrosis. Likewise, we present a review of the current diagnostic and therapeutic management of patients with MEN1 syndrome who are diagnosed with thymic carcinoid.