Swyer-James-MacLeod Syndrome in a Patient with Eisenmenger Syndrome

• Published in: Turk Kardiyoloji Dernegi arsivi : Turk Kardiyoloji Derneginin yayin organidir Vol. 52; no. 6; pp. 460 - 463
• Main Authors: Gürses, Dolunay, Oğuz, Merve, Yüksel, Doğangün, Ufuk, Furkan, Yılmaz, Münevver
• Format: Journal Article
• Language: English
• Published: Turkey 01-09-2024
• Subjects: Adult; Diagnosis, Differential; Eisenmenger Complex - complications; Eisenmenger Complex - diagnostic imaging; Humans; Lung, Hyperlucent - complications; Lung, Hyperlucent - diagnosis; Lung, Hyperlucent - diagnostic imaging; Male; Tomography, X-Ray Computed
• ISSN: 1016-5169; 1308-4488
• DOI: 10.5543/tkda.2023.59829

Swyer-James-MacLeod syndrome is characterized radiologically by hyperlucency in a single lung lobe, accompanied by reduced vascularity, alveolar hyperdistention, and air trapping, without bronchial airway obstruction. The most common congenital heart defect in childhood, ventricular septal defect, leads to irreversible pulmonary hypertension and Eisenmenger syndrome if not treated promptly. This case report presents a 25-year-old patient with Swyer-James-MacLeod syndrome and Eisenmenger syndrome. It is crucial to include Swyer-James-MacLeod syndrome in the differential diagnosis of patients with atypically distributed pulmonary emphysema and unilateral hyperlucency for early diagnosis and timely intervention.