THE COMBINATION OF ANNULAR PANCREAS, PARASTERNAL DIAPHRAGMATIC HERNIA IN A NEWBORN WITH DOWN SYNDROME

• Published in: Vestnik hirurgii im. I.I. Grekova Vol. 177; no. 4; pp. 44 - 46
• Main Authors: Aksel’rov, M. A., Emel’janov, V. A.
• Format: Journal Article
• Language: English; Russian
• Published: Pavlov First Saint Petersburg State Medical University 08-09-2018
• Subjects: annular pancreas; chyloperitoneum; diaphragmatic hernia; down syndrome; octreotide
• ISSN: 0042-4625
• DOI: 10.24884/0042-4625-2018-177-4-44-46

Malformations  and  premature birth are  the  most  important  causes of chronic  diseases, disability and  mortality in childhood. Help  for  children   with  malformations  is  often  needed immediately   after  birth.  WHO  determines heart   defects,  neural tube   defects,  chromosomal  abnormality –  Down  syndrome as  the  most   severe  malformations. Down  syndrome  is  a genetic disease in which the child has the superfluous chromosome and often defects in the development of different organs and   systems. The  presence of  several defects  requires a  complex   surgical   approach that  can   be  performed endoscopically.  It  is  known  that  Down  syndrome  can   be  combined  with  chyloperitoneum.  The  article  represents  the clinical  observation  of  successful  treatment  of  the   newborn  baby   with  Down  syndrome,  which  was   combined  with congenital high  intestinal  obstruction at  the  level  of the  duodenum and  parasternal  diaphragmatic hernia, both  defects were corrected laparoscopically. The chyloperitoneum developed in postoperative period was successfully treated with the appointment of total parenteral nutrition and infusions of Sandostatin analogues.