A Radiological Curiosity of a Rare Diagnosis: Lhermitte-Duclos Disease

• Published in: Asian journal of oncology Vol. 8; no. 3; pp. 136 - 139
• Main Authors: Wilson Bizimana, Rita Oze Koudouhonon, Suzanne Rita Aubin Igombe, Waïs A. Amarkak, Khadija Benelhosni, Ittimade Nassar, Nabil Billah Moatassim
• Format: Journal Article
• Language: English
• Published: Thieme Medical Publishers, Inc 17-10-2022
• Subjects: cerebellum; lhermitte duclos disease; tiger striping sign
• DOI: 10.1055/s-0042-1748638
• EISSN: 2455-4618
• ISSN: 2454-6798

Lhermitte–Duclos disease (LDD) is a rare cerebellar lesion, described in 1920 by two French physicians: Lhermitte and Duclos. The clinical presentation is usually made of neurological symptoms. This lesion is characterized by a hamartomatous lesion in the posterior fossa. Mainly diagnosed by MRI, when it comes to preoperative, the T2-weightened MRI demonstrates the classical “tiger-striped” pattern. The definitive diagnosis, nonetheless, is histopathological. The treatment for LDD consists of surgical decompression or excision. We present here a rare case of a woman who developed neurological symptoms that led to LDD diagnosis to describe protocol MRI imaging, the main findings and their pathophysiological meanings.